Abstract
gamma-Secretase is a membrane-associated protease that cleaves within the transmembrane region of amyloid precursor protein to generate the C termini of the two Abeta peptide isoforms, Abeta40 and Abeta42. Here we report the detergent solubilization and partial characterization of gamma-secretase. The activity of solubilized gamma-secretase was measured with a recombinant substrate, C100Flag, consisting largely of the C-terminal fragment of amyloid precursor protein downstream of the beta-secretase cleavage site. Cleavage of C100Flag by gamma-secretase was detected by electrochemiluminescence using antibodies that specifically recognize the Abeta40 or Abeta42 termini. Incubation of C100Flag with HeLa cell membranes or detergent-solubilized HeLa cell membranes generates both the Abeta40 and Abeta42 termini. Recovery of catalytically competent, soluble gamma-secretase critically depends on the choice of detergent; CHAPSO (3-[(3-cholamidopropyl)dimethylammonio]-2-hydroxy-1-propanesulfonate) but not Triton X-100 is suitable. Solubilized gamma-secretase activity is inhibited by pepstatin and more potently by a novel aspartyl protease transition-state analog inhibitor that blocks formation of Abeta40 and Abeta42 in mammalian cells. Upon gel exclusion chromatography, solubilized gamma-secretase activity coelutes with presenilin 1 (PS1) at an apparent relative molecular weight of approximately 2.0 x 10(6). Anti-PS1 antibody immunoprecipitates gamma-secretase activity from the solubilized gamma-secretase preparation. These data suggest that gamma-secretase activity is catalyzed by a PS1-containing macromolecular complex.
MeSH Terms
Alzheimer Disease/enzymology
Amyloid Precursor Protein Secretases
Amyloid beta-Protein Precursor/metabolism
Aspartic Acid Endopeptidases
Carbamates/pharmacology
Cell Fractionation/methods
Cell Membrane/chemistry
Cholic Acids/pharmacology
Detergents/pharmacology
Dipeptides/pharmacology
Endopeptidases/chemistry,immunology,isolation & purification
HeLa Cells/chemistry,drug effects
Humans
Membrane Proteins/chemistry,immunology,isolation & purification
Neoplasm Proteins/isolation & purification
Pepstatins/pharmacology
Presenilin-1
Protease Inhibitors/pharmacology
Recombinant Fusion Proteins/metabolism
Solubility
Substrate Specificity
Chemicals
Amyloid beta-Protein Precursor
Carbamates
Cholic Acids
Detergents
Dipeptides
L 685458
Membrane Proteins
Neoplasm Proteins
PSEN1 protein, human
Pepstatins
Presenilin-1
Protease Inhibitors
Recombinant Fusion Proteins
Streptomyces pepsin inhibitor
chapso
Amyloid Precursor Protein Secretases
Endopeptidases
Aspartic Acid Endopeptidases
BACE1 protein, human
3-((3-cholamidopropyl)dimethylammonium)-1-propanesulfonate
pepstatin
Authors & Affiliations
10 authors, click to expand affiliations / ORCID
Li Y M
Department of Biological Chemistry, Merck Research Laboratories, West Point, PA 19486, USA.
[email protected]
Lai M T
Xu M
Huang Q
DiMuzio-Mower J
Sardana M K
Shi X P
Yin K C
Shafer J A
Gardell S J
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