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PMID: 19126569 Published · ppublish English Clinical Trial Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

A pilot open label, single dose trial of fenobam in adults with fragile X syndrome.

Journal of medical genetics ·Vol. 46 ·No. 4 ·2009-04-00 ·Pages 266-71

Berry-Kravis E, Hessl D, Coffey S, Hervey C, Schneider A, Yuhas J, Hutchison J, Snape M, Tranfaglia M, Nguyen DV, Hagerman R

Abstract

A pilot open label, single dose trial of fenobam, an mGluR5 antagonist, was conducted to provide an initial evaluation of safety and pharmacokinetics in adult males and females with fragile X syndrome (FXS). Twelve subjects, recruited from two fragile X clinics, received a single oral dose of 50-150 mg of fenobam. Blood for pharmacokinetic testing, vital signs and side effect screening was obtained at baseline and numerous time points for 6 h after dosing. Outcome measures included prepulse inhibition (PPI) and a continuous performance test (CPT) obtained before and after dosing to explore the effects of fenobam on core phenotypic measures of sensory gating, attention and inhibition. There were no significant adverse reactions to fenobam administration. Pharmacokinetic analysis showed that fenobam concentrations were dose dependent but variable, with mean (SEM) peak values of 39.7 (18.4) ng/ml at 180 min after the 150 mg dose. PPI met a response criterion of an improvement of at least 20% over baseline in 6 of 12 individuals (4/6 males and 2/6 females). The CPT did not display improvement with treatment due to ceiling effects. Clinically significant adverse effects were not identified in this study of single dose fenobam across the range of dosages utilised. The positive effects seen in animal models of FXS treated with fenobam or other mGluR5 antagonists, the apparent lack of clinically significant adverse effects, and the potential beneficial clinical effects seen in this pilot trial support further study of the compound in adults with FXS.

MeSH Terms
Administration, Oral Adolescent Adult Chromatography, Liquid Female Fragile X Syndrome/metabolism,physiopathology,psychology Humans Imidazoles/administration & dosage,blood,pharmacokinetics Inhibition, Psychological Male Mass Spectrometry Neural Inhibition/drug effects Neuropsychological Tests Pilot Projects Receptor, Metabotropic Glutamate 5 Receptors, Metabotropic Glutamate/antagonists & inhibitors Young Adult
Chemicals
GRM5 protein, human Imidazoles Receptor, Metabotropic Glutamate 5 Receptors, Metabotropic Glutamate fenobam
Authors & Affiliations
11 authors, click to expand affiliations / ORCID
Berry-Kravis E
Departments of Pediatrics, Rush University Medical Center, 1725 West Harrison Street, Suite 718, Chicago, IL 60612, USA. [email protected]
Hessl D
Coffey S
Hervey C
Schneider A
Yuhas J
Hutchison J
Snape M
Tranfaglia M
Nguyen D V
Hagerman R
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Article Info
Journal
Journal of medical genetics
Abbr.
J Med Genet
ISSN
1468-6244
Published
2009-04-00
Epub
2009-00-06
Pages
266-71
Language
English
Region
England
NLM ID
2985087R
PMCID
PMC2658751
Subset
IM
Grants
NIMH NIH HHS · K23 MH077554 · United States
NIDCR NIH HHS · UL1 DE019583 · United States
NIMH NIH HHS · MH77554 · United States
NCRR NIH HHS · UL1RR024146 · United States
NIA NIH HHS · RL1AG032119 · United States
NCBDD CDC HHS · U50 DD000596 · United States
NIA NIH HHS · RL1AG032115 · United States
NCRR NIH HHS · UL1 RR024146 · United States
NIA NIH HHS · RL1 AG032119 · United States
NIA NIH HHS · RL1 AG032115 · United States
NICHD NIH HHS · R01 HD036071 · United States
NICHD NIH HHS · HD036071 · United States
NIDCR NIH HHS · UL1DE019583 · United States
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