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PMID: 22331816 Published · ppublish English Journal Article Research Support, N.I.H., Extramural

Phenotypic information in genomic variant databases enhances clinical care and research: the International Standards for Cytogenomic Arrays Consortium experience.

Human mutation ·Vol. 33 ·No. 5 ·2012-05-00 ·Pages 787-96

Riggs ER, Jackson L, Miller DT, Van Vooren S

Abstract

Whole-genome analysis, now including whole-genome sequencing, is moving rapidly into the clinical setting, leading to detection of human variation on a broader scale than ever before. Interpreting this information will depend on the availability of thorough and accurate phenotype information, and the ability to curate, store, and access data on genotype-phenotype relationships. This idea has already been demonstrated within the context of chromosomal microarray (CMA) testing. The International Standards for Cytogenomic Arrays (ISCA) Consortium promotes standardization of variant interpretation for this technology through its initiatives, including the formation of a publicly available database housing clinical CMA data. Recognizing that phenotypic data are essential for the interpretation of genomic variants, the ISCA Consortium has developed tools to facilitate the collection of these data and its deposition in a standardized structured format within the ISCA Consortium database. This rich source of phenotypic data can also be used within broader applications such as developing phenotypic profiles of emerging genomic disorders, identification of candidate regions for particular phenotypes, or creation of tools for use in clinical practice. We summarize the ISCA experience as a model for ongoing efforts incorporating phenotype data with genotype data to improve the quality of research and clinical care in human genetics.

MeSH Terms
Cytogenetic Analysis Data Mining Databases, Genetic Genetic Association Studies Genetic Variation Genome-Wide Association Study Humans Medical Informatics Phenotype Precision Medicine
Authors & Affiliations
4 authors, click to expand affiliations / ORCID
Riggs Erin Rooney
Department of Human Genetics, Emory University School of Medicine, Atlanta, Georgia, USA. [email protected]
Jackson Laird
Miller David T
Van Vooren Steven
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Article Info
Journal
Human mutation
Abbr.
Hum Mutat
ISSN
1098-1004
Published
2012-05-00
Epub
2012-00-20
Pages
787-96
Language
English
Region
United States
NLM ID
9215429
PMCID
PMC3327820
Subset
IM
Grants
NICHD NIH HHS · RC2 HD064525 · United States
NICHD NIH HHS · RC2 HD064525-01 · United States
NICHD NIH HHS · HD064525 · United States
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