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PMID: 29681546 Published · ppublish English Journal Article Review

EDUCATIONAL SERIES IN CONGENITAL HEART DISEASE: Congenital left-sided heart obstruction.

Echo research and practice ·Vol. 5 ·No. 2 ·2018-06-00 ·Pages R23-R36

Carr M, Curtis S, Marek J

Abstract

Congenital obstruction of the left ventricular outflow tract remains a significant problem and multilevel obstruction can often coexist. Obstruction can take several morphological forms and may involve the subvalvar, valvar or supravalvar portion of the aortic valve complex. Congenital valvar stenosis presenting in the neonatal period represents a spectrum of disorders ranging from the hypoplastic left heart syndrome to almost normal hearts. Treatment options vary dependent on the severity of the left ventricular outflow tract obstruction (LVOTO) and the variable degree of left ventricular hypoplasia as well as the associated lesions such as arch hypoplasia and coarctation.

Keywords
aortic stenosis bicuspid aortic valve coarctation of the aorta congenital heart defects left ventricular outflow tract obstruction
Authors & Affiliations
3 authors, click to expand affiliations / ORCID
Carr Michelle
Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK.
Curtis Stephanie
Bristol Heart Institute, University Hospitals Bristol, Bristol, UK.
Marek Jan
Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK. | Institute of Cardiovascular Sciences, University College London, London, UK.
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Article Info
Journal
Echo research and practice
Abbr.
Echo Res Pract
ISSN
2055-0464
DOI
10.1530/ERP-18-0016
Published
2018-06-00
Epub
2018-00-16
Pages
R23-R36
Language
English
Region
England
NLM ID
101664713
PMCID
PMC5911774
External Links
PubMed source DOI: 10.1530/ERP-18-0016 PMC Full Text View journal details
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