Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects.

Amino Acid Sequence Cell Nucleus/metabolism Cloning, Molecular Energy Metabolism Enzymes/genetics,metabolism Humans Metabolism, Inborn Errors/genetics,metabolism Mitochondria/metabolism Models, Biological Ornithine Carbamoyltransferase/genetics,metabolism Protein Sorting Signals/genetics,metabolism Proteins/genetics,metabolism

Enzymes Protein Sorting Signals Proteins Ornithine Carbamoyltransferase