Brain sphingolipids in I cell disease (mucolipidosis II).

Abnormalities, Multiple/metabolism Ceramides/analysis Cerebrosides/analysis Child, Preschool Chromatography, Gas Chromatography, Thin Layer Cytoplasmic Granules Fibroblasts Galactose Gangliosides/analysis Glucose Humans Lactose Lipidoses/metabolism Mucopolysaccharidosis I/metabolism Mucopolysaccharidosis II/metabolism Neuraminic Acids/analysis Retinitis Pigmentosa/metabolism Sphingolipids/analysis Sphingomyelins/analysis Sulfoglycosphingolipids/analysis Syndrome

Ceramides Cerebrosides Gangliosides Neuraminic Acids Sphingolipids Sphingomyelins Sulfoglycosphingolipids Glucose Lactose Galactose