Congenital Atrophic Dermatofibrosarcoma Protuberans: A Case Report and Narrative Review of the Literature.

Dermatofibrosarcoma protuberans is a rare dermal and subcutaneous soft-tissue tumor, uncommon in children, characterized by CD34 positivity and COL1A1-PDGFB fusion. Prognosis is generally good, but local recurrence risk is high, so complete excision with clear margins and six-monthly follow-up for three years after surgery is recommended in most cases.