Nigro-spino-dentatal degeneration with nuclear ophthalmoplegia. A unique and partially treatable clinico-pathological entity.

Adult Aged Ataxia/complications,genetics,pathology Basal Ganglia Diseases/complications,genetics Cerebellar Diseases/complications,genetics,pathology Cerebellar Nuclei/pathology Female Genes, Dominant Humans Male Middle Aged Nerve Degeneration Oculomotor Nerve/pathology Ophthalmoplegia/complications,genetics,pathology Pedigree Spinal Cord/pathology Spinal Cord Diseases/complications,genetics,pathology Substantia Nigra/pathology Tegmentum Mesencephali/pathology