Abstract
We report a mother and daughter with features of the velocardiofacial (VCF) syndrome and monosomy for 22q11 identified using molecular techniques. The mother had surgery as a child for a cleft palate and a congenital heart defect, and her facial features were consistent with the diagnosis. The daughter had developmental delay, absent speech, scoliosis, and similar facial features, but no cleft palate or congenital heart defect. These cases illustrate the considerable intrafamilial variability of the phenotype of VCF syndrome. The clinical and molecular diagnosis of this syndrome is discussed. The phenotypic variability of the VCF syndrome means that many cases may be undiagnosed.
MeSH Terms
Abnormalities, Multiple/genetics,pathology
Child
Chromosome Deletion
Cleft Palate/genetics
Face/abnormalities
Female
Gene Deletion
Genetic Variation
Heart Defects, Congenital/genetics,pathology
Humans
Monosomy
Neurocognitive Disorders/genetics
Phenotype
Syndrome
Velopharyngeal Insufficiency/genetics,pathology
Authors & Affiliations
4 authors, click to expand affiliations / ORCID
Holder S E
Mothercare Unit of Clinical Genetics and Fetal Medicine, Institute of Child Health, London, UK.
Winter R M
Kamath S
Scambler P J
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