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PMID: 8312368 Published · ppublish English Journal Article Review

The Niemann-Pick C lesion and its relationship to the intracellular distribution and utilization of LDL cholesterol.

Biochimica et biophysica acta ·Vol. 1225 ·No. 3 ·1994-02-22 ·Pages 235-43

Pentchev PG, Brady RO, Blanchette-Mackie EJ, Vanier MT, Carstea ED, Parker CC, Goldin E, Roff CF

Abstract

暂无摘要

MeSH Terms
Animals Biological Transport Cholesterol/metabolism Cholesterol Esters/metabolism Cholesterol, LDL/metabolism Fibroblasts/metabolism Humans Liver/metabolism Niemann-Pick Diseases/etiology,metabolism Receptors, LDL/metabolism Subcellular Fractions/metabolism
Chemicals
Cholesterol Esters Cholesterol, LDL Receptors, LDL Cholesterol
Authors & Affiliations
8 authors, click to expand affiliations / ORCID
Pentchev P G
Molecular and Cellular Pathophysiology Section, National Institute of Neurological Disorders and Stroke, National Institutes of Health, Bethesda, MD 20892.
Brady R O
Blanchette-Mackie E J
Vanier M T
Carstea E D
Parker C C
Goldin E
Roff C F
Article Info
Journal
Biochimica et biophysica acta
Abbr.
Biochim Biophys Acta
ISSN
0006-3002
Published
1994-02-22
Pages
235-43
Language
English
Region
Netherlands
NLM ID
0217513
Subset
IM
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