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PMID: 9837821 Published · ppublish English Journal Article Research Support, Non-U.S. Gov't Research Support, U.S. Gov't, P.H.S.

The Ashkenazic Jewish Bloom syndrome mutation blmAsh is present in non-Jewish Americans of Spanish ancestry.

American journal of human genetics ·Vol. 63 ·No. 6 ·1998-12-00 ·Pages 1685-93

Ellis NA, Ciocci S, Proytcheva M, Lennon D, Groden J, German J

Abstract

Bloom syndrome (BS) is more frequent in the Ashkenazic Jewish population than in any other. There the predominant mutation, referred to as "blmAsh," is a 6-bp deletion and 7-bp insertion at nucleotide position 2281 in the BLM cDNA. Using a convenient PCR assay, we have identified blmAsh on 58 of 60 chromosomes transmitted by Ashkenazic parents to persons with BS. In contrast, in 91 unrelated non-Ashkenazic persons with BS whom we examined, blmAsh was identified only in 5, these coming from Spanish-speaking Christian families from the southwestern United States, Mexico, or El Salvador. These data, along with haplotype analyses, show that blmAsh was independently established through a founder effect in Ashkenazic Jews and in immigrants to formerly Spanish colonies. This striking observation underscores the complexity of Jewish history and demonstrates the importance of migration and genetic drift in the formation of human populations.

MeSH Terms
Adenosine Triphosphatases/genetics Alleles Bloom Syndrome/ethnology,genetics Christianity Chromosomes, Human Consanguinity DNA Helicases/genetics El Salvador Founder Effect Gene Frequency Genotype Haplotypes Humans Jews/genetics Mexico Mutation Polymerase Chain Reaction Polymorphism, Genetic RecQ Helicases Spain/ethnology United States
Chemicals
Adenosine Triphosphatases Bloom syndrome protein DNA Helicases RecQ Helicases
Authors & Affiliations
6 authors, click to expand affiliations / ORCID
Ellis N A
Department of Human Genetics, Memorial Sloan-Kettering Cancer Center, 1275 York Avenue, USA. [email protected]
Ciocci S
Proytcheva M
Lennon D
Groden J
German J
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14 references, click to expand
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Article Info
Journal
American journal of human genetics
Abbr.
Am J Hum Genet
ISSN
0002-9297
Published
1998-12-00
Pages
1685-93
Language
English
Region
United States
NLM ID
0370475
PMCID
PMC1377640
Subset
IM
Grants
NCI NIH HHS · CA50897 · United States
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