Home LiteratureArticle Details
PMID: 9151717 Published · ppublish English Journal Article Research Support, U.S. Gov't, P.H.S.

Suppression of cathepsins B and L causes a proliferation of lysosomes and the formation of meganeurites in hippocampus.

Bednarski E, Ribak CE, Lynch G

Abstract

Cultured hippocampal slices exhibited prominent ultrastructural features of brain aging after exposure to an inhibitor of cathepsins B and L. Six days of treatment with N-CBZ-L-phenylalanyl-L-alanine-diazomethylketone (ZPAD) resulted in a dramatic increase in the number of lysosomes in the perikarya of neurons and glial cells throughout the slices. Furthermore, lysosomes in CA1 and CA3 pyramidal cells were not restricted to the soma but instead were located throughout dendritic processes. Clusters of lysosomes were commonly found within bulging segments of proximal dendrites that were notable for an absence of microtubules and neurofilaments. Although pyknotic nuclei were sometimes encountered, most of the cells in slices exposed to ZPAD for 6 d appeared relatively normal. Slices given 7 d of recovery contained several unique features, compared with those processed immediately after incubation with the inhibitor. Cell bodies of CA1 neurons were largely cleared of the excess lysosomes but had gained fusiform, somatic extensions that were filled with fused lysosomes and related complex, dense bodies. These appendages, similar in form and content to structures previously referred to as "meganeurites," were not observed in CA3 neurons or granule cells. Because meganeurites were often interposed between cell body and axon, they have the potential to interfere with processes requiring axonal transport. It is suggested that inactivation of cathepsins B and L results in a proliferation of lysosomes and that meganeurite generation provides a means of storing residual catabolic organelles. The accumulated material could be eliminated by pinching off the meganeurite but, at least in some cases, this action would result in axotomy. Reduced cathepsin L activity, increased numbers of lysosomes, and the formation of meganeurites are all reported to occur during brain aging; thus, it is possible that the infusion of ZPAD into cultured slices sets in motion a greatly accelerated gerontological sequence.

MeSH Terms
Animals Cathepsin B/antagonists & inhibitors,metabolism Cathepsin L Cathepsins/antagonists & inhibitors,metabolism Cysteine Endopeptidases Cysteine Proteinase Inhibitors/pharmacology Diazomethane/analogs & derivatives,pharmacology Endopeptidases Enzyme Precursors/antagonists & inhibitors,metabolism Hippocampus/cytology,metabolism Hydrolases/analysis,metabolism Lysosomes/drug effects,enzymology Microscopy, Electron Nerve Degeneration/drug effects,physiology Neurites/drug effects,physiology,ultrastructure Organ Culture Techniques Pyramidal Cells/cytology,physiology,ultrastructure Rats Rats, Sprague-Dawley
Chemicals
Cysteine Proteinase Inhibitors Enzyme Precursors benzyloxycarbonylphenylalanylalanine diazomethyl ketone Diazomethane Hydrolases Cathepsins Endopeptidases Cysteine Endopeptidases Cathepsin B Cathepsin L Ctsl protein, rat
Authors & Affiliations
3 authors, click to expand affiliations / ORCID
Bednarski E
Center for the Neurobiology of Learning and Memory, University of California, Irvine, California 92697, USA.
Ribak C E
Lynch G
References (61)
61 references, click to expand
  1. Cytosolic proteolysis of tau by cathepsin D in hippocampus following suppression of cathepsins B and L.
    J Neurochem. 1996 Nov;67(5):1846-55 PMID: 8863489
  2. Participation of cathepsin L on bone resorption.
    FEBS Lett. 1993 Apr 26;321(2-3):247-50 PMID: 8477857
  3. Neuronal aging in cultures. An electron-microscopic study.
    Exp Gerontol. 1973 Oct;8(5):259-63 PMID: 4767689
  4. Fine structure of meganeurites and secondary growth processes in feline GM1-gangliosidosis.
    Brain Res. 1978 Mar 17;143(1):1-12 PMID: 415797
  5. Inhibitors of lysosomal enzymes: accumulation of lipofuscin-like dense bodies in the brain.
    Science. 1984 Nov 23;226(4677):985-7 PMID: 6505679
  6. Quantitative synaptic alterations in the human neocortex during normal aging.
    Neurology. 1993 Jan;43(1):192-7 PMID: 8423884
  7. Evidence for decreased transport of tryptophan hydroxylase in Alzheimer's disease.
    Brain Res. 1990 Dec 24;537(1-2):83-7 PMID: 1707735
  8. Translational suppression of calpain I reduces NMDA-induced spectrin proteolysis and pathophysiology in cultured hippocampal slices.
    Brain Res. 1995 Oct 2;694(1-2):147-57 PMID: 8974639
  9. Cleavage of structural proteins during the assembly of the head of bacteriophage T4.
    Nature. 1970 Aug 15;227(5259):680-5 PMID: 5432063
  10. Ultrastructural observations on neuronal lipofuscin (age pigment) and dense bodies induced by a proteinase inhibitor, leupeptin, in rat hippocampus.
    Acta Neuropathol. 1993;86(4):319-28 PMID: 8256581
  11. Delineation of chicken cathepsin L secondary structure; relationship between pH dependence activity and helix content.
    Biochim Biophys Acta. 1988 Jun 29;955(1):58-64 PMID: 3382672
  12. A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding.
    Anal Biochem. 1976 May 7;72:248-54 PMID: 942051
  13. Distortion of neuronal geometry and formation of aberrant synapses in neuronal storage disease.
    Brain Res. 1976 Oct 29;116(1):1-21 PMID: 824017
  14. Cathepsin B, Cathepsin H, and cathepsin L.
    Methods Enzymol. 1981;80 Pt C:535-61 PMID: 7043200
  15. The amount and distribution of pigments in neurons and glia of the cerebral cortex. Autofluorescent and ultrastructural studies.
    J Gerontol. 1969 Apr;24(2):127-35 PMID: 5789243
  16. Enzymatically active lysosomal proteases are associated with amyloid deposits in Alzheimer brain.
    Proc Natl Acad Sci U S A. 1990 May;87(10):3861-5 PMID: 1692625
  17. Structural modifications associated with synaptic development in area CA1 of rat hippocampal organotypic cultures.
    Brain Res Dev Brain Res. 1993 Jan 15;71(1):81-91 PMID: 8432003
  18. Identification of a novel microtubule binding and assembly domain in the developmentally regulated inter-repeat region of tau.
    J Cell Biol. 1994 Mar;124(5):769-82 PMID: 8120098
  19. The effect of protease inhibitors and decreased temperature on the degradation of different classes of proteins in cultured hepatocytes.
    J Cell Physiol. 1979 Dec;101(3):439-57 PMID: 528571
  20. beta-Amyloid precursor protein fragments and lysosomal dense bodies are found in rat brain neurons after ventricular infusion of leupeptin.
    Brain Res. 1994 Mar 21;640(1-2):25-32 PMID: 8004453
  21. A simple method for organotypic cultures of nervous tissue.
    J Neurosci Methods. 1991 Apr;37(2):173-82 PMID: 1715499
  22. Pigmentoarchitectonic pathology of the isocortex in juvenile neuronal ceroid-lipofuscinosis: axonal enlargements in layer IIIab and cell loss in layer V.
    Acta Neuropathol. 1979 Apr 12;46(1-2):79-83 PMID: 452864
  23. Protease inhibition causes some manifestations of aging and Alzheimer's disease in rodent and primate brain.
    Ann N Y Acad Sci. 1992 Dec 31;674:89-102 PMID: 1337691
  24. Comparative behaviour of calpain and cathepsin B toward peptidyl acyloxymethyl ketones, sulphonium methyl ketones and other potential inhibitors of cysteine proteinases.
    Biochem J. 1992 Dec 15;288 ( Pt 3):759-62 PMID: 1471990
  25. Proteases and proteolysis in the lysosome.
    Experientia. 1992 Feb 15;48(2):151-7 PMID: 1740187
  26. Studies on the mechanisms of autophagy: maturation of the autophagic vacuole.
    J Cell Biol. 1990 Jun;110(6):1935-45 PMID: 2161853
  27. Induction of beta-amyloid-containing polypeptides in hippocampus: evidence for a concomitant loss of synaptic proteins and interactions with an excitotoxin.
    Exp Neurol. 1994 Sep;129(1):81-94 PMID: 7925845
  28. ULTRASTRUCTURAL STUDIES IN ALZHEIMER'S PRESENILE DEMENTIA.
    Am J Pathol. 1964 Feb;44:269-97 PMID: 14119171
  29. Age-related changes in activities and localizations of cathepsins D, E, B, and L in the rat brain tissues.
    Exp Neurol. 1994 Mar;126(1):119-28 PMID: 8157122
  30. Routes of excretion of neuronal lysosomal dense bodies after ventricular infusion of leupeptin in the rat: a study using ubiquitin and PGP 9.5 immunocytochemistry.
    J Neurocytol. 1993 Sep;22(9):779-91 PMID: 8270961
  31. Lysosomal abnormalities in degenerating neurons link neuronal compromise to senile plaque development in Alzheimer disease.
    Brain Res. 1994 Mar 21;640(1-2):68-80 PMID: 8004466
  32. The selective role of cathepsins B and D in the lysosomal degradation of endogenous and exogenous proteins.
    FEBS Lett. 1991 Aug 5;287(1-2):189-92 PMID: 1715285
  33. A time-lapse video image intensification analysis of cytoplasmic organelle movements during endosome translocation.
    J Cell Biol. 1984 Feb;98(2):565-76 PMID: 6693496
  34. Lipofuscin-like substances accumulate rapidly in brain, retina and internal organs with cysteine protease inhibition.
    Adv Exp Med Biol. 1989;266:31-45; discussion 45-7 PMID: 2486158
  35. Cathepsin L--a lysosomal cysteine proteinase.
    Prog Clin Biol Res. 1985;180:61-9 PMID: 4034565
  36. Gene expression and cellular content of cathepsin D in Alzheimer's disease brain: evidence for early up-regulation of the endosomal-lysosomal system.
    Neuron. 1995 Mar;14(3):671-80 PMID: 7695914
  37. Functions of lysosomes.
    Annu Rev Physiol. 1966;28:435-92 PMID: 5322983
  38. Characterization of tau protein present in microtubules and paired helical filaments of Alzheimer's disease patient's brain.
    Neuroscience. 1990;37(1):163-70 PMID: 2123019
  39. Translational suppression of calpain blocks long-term potentiation.
    Learn Mem. 1996 Sep-Oct;3(2-3):209-17 PMID: 10456091
  40. Properties of the endosomal-lysosomal system in the human central nervous system: disturbances mark most neurons in populations at risk to degenerate in Alzheimer's disease.
    J Neurosci. 1996 Jan;16(1):186-99 PMID: 8613784
  41. Increase in cathepsin D activity in rat brain in aging.
    J Neurosci Res. 1989 Aug;23(4):454-6 PMID: 2769800
  42. Electron microscopical studies on rat brain neurons. Localization of acid phosphatase and mode of formation of lipofuscin bodies.
    J Ultrastruct Res. 1972 Jan;38(1):1-15 PMID: 4333274
  43. Intraventricular infusion of leupeptin decreases Bmax of the D2 receptor in the striatum of young rats.
    Life Sci. 1992;50(19):1451-7 PMID: 1533437
  44. Aging in the rat olfactory bulb: quantitative changes in mitral cell organelles and somato-dendritic synapses.
    J Comp Neurol. 1979 Apr 15;184(4):811-20 PMID: 422764
  45. Time course of synaptic development in hippocampal organotypic cultures.
    Brain Res Dev Brain Res. 1993 Jan 15;71(1):93-100 PMID: 8432004
  46. Dendritic transport. II. Somatofugal movement of neuronal lysosomes induced by colchicine: evidence for a novel transport system in dendrites.
    J Neurosci. 1985 Aug;5(8):2018-27 PMID: 4020430
  47. Induction of calpain-mediated spectrin fragments by pathogenic treatments in long-term hippocampal slices.
    J Pharmacol Exp Ther. 1995 May;273(2):902-8 PMID: 7538583
  48. Cytoskeletal changes in rat cortical neurons induced by long-term intraventricular infusion of leupeptin.
    Acta Neuropathol. 1995;89(1):8-16 PMID: 7709735
  49. Lysosome instability in aged rat brain.
    Neurosci Lett. 1989 Feb 13;97(1-2):215-20 PMID: 2919004
  50. A protein factor essential for microtubule assembly.
    Proc Natl Acad Sci U S A. 1975 May;72(5):1858-62 PMID: 1057175
  51. Stable maintenance of glutamate receptors and other synaptic components in long-term hippocampal slices.
    Hippocampus. 1995;5(5):425-39 PMID: 8773255
  52. Inhibition of proteolysis protects hippocampal neurons from ischemia.
    Proc Natl Acad Sci U S A. 1991 Aug 15;88(16):7233-7 PMID: 1871130
  53. Differences in the pattern of hippocampal neuronal loss in normal ageing and Alzheimer's disease.
    Lancet. 1994 Sep 17;344(8925):769-72 PMID: 7916070
  54. Anomalous accumulation of tau and ubiquitin immunoreactivities in rat brain caused by protease inhibition and by normal aging: a clue to PHF pathogenesis?
    Brain Res. 1989 Oct 2;498(2):360-5 PMID: 2477115
  55. The effects of aging on area 46 of the frontal cortex of the rhesus monkey.
    Cereb Cortex. 1994 Nov-Dec;4(6):621-35 PMID: 7703688
  56. Specific assay method for the activities of cathepsin L-type cysteine proteinases.
    J Biochem. 1994 Aug;116(2):282-4 PMID: 7822244
  57. Spindle-shaped appendages of IIIab-pyramids filled with lipofuscin: a striking pathological change of the senescent human isocortex.
    Acta Neuropathol. 1979 May 15;46(3):197-202 PMID: 463497
  58. INTRACELLULAR LOCALIZATION OF LIPOFUSCIN AGE PIGMENTS IN THE NERVOUS SYSTEM.
    J Gerontol. 1964 Jul;19:262-76 PMID: 14179681
  59. Peptidyl diazomethyl ketones are specific inactivators of thiol proteinases.
    J Biol Chem. 1981 Feb 25;256(4):1923-8 PMID: 7007374
  60. Lipoprotein pigments--their relationship to ageing in the human nervous system. I. The lipofuscin content of nerve cells.
    Brain. 1974 Sep;97(3):481-8 PMID: 4423477
  61. Inhibition of proteolytic activity of calcium activated neutral protease by leupeptin and antipain.
    Biochem Biophys Res Commun. 1978 May 30;82(2):484-91 PMID: 666855
Article Info
Journal
The Journal of neuroscience : the official journal of the Society for Neuroscience
Abbr.
J Neurosci
ISSN
0270-6474
Published
1997-06-01
Pages
4006-21
Language
English
Region
United States
NLM ID
8102140
PMCID
PMC6573562
Subset
IM
Grants
NIA NIH HHS · AG00538 · United States
NIMH NIH HHS · MH14599 · United States
Analysis Services
Analysis Services

Contact

No. 2 Wenbo Road, Zhangqiu District, Jinan, Shandong

Qilu Normal University · Genelibs Bioinformatics Lab

750 Shunhua Rd, Jinan

2F, Bldg F, University Science Park

Tel: 0531-88819269

WeChat Official Account

Follow our WeChat subscription account for real-time updates and the latest in medical and biological research.


Business Email

E-mail: [email protected]